Endocrine and Neuroendocrine Tumours

Pituitary gland

              Introduction

    Anterior neuroendocrine neoplasms

         Pituitary neuroendocrine tumors of PIT1-lineage
              Somatotroph PitNET/adenoma
              Mammosomatotroph PitNET/adenoma
              Lactotroph PitNET/adenoma
              Thyrotroph PitNET/adenoma
              Mature plurihormonal PIT1 lineage PitNET/adenoma
              Immature PIT1-lineage PitNET/adenoma
              Acidophil stem cell PitNET/adenoma
              Mixed somatotroph-lactotroph PitNET/adenoma
         Pituitary neuroendocrine tumors of TPIT lineage
              Corticotroph PitNET/adenoma
         Pituitary neuroendocrine tumors of SF1 lineage
              Gonadotroph PitNET/adenoma
         Pituitary neuroendocrine tumours without distinct lineage differentiation
              Null cell PitNET/adenoma
              Plurihormonal PitNET/adenomas
         Multiple pituitary neuroendocrine tumours
              Multiple synchronous PitNET/adenomas of distinct lineages
         Metastatic pituitary neuroendocrine tumours
              Metastatic PitNET

    Other anterior pituitary tumours

              Adamantinomatous craniopharyngioma
              Papillary craniopharyngioma
              Pituitary blastoma

    Posterior pituitary and hypothalamic neoplasms

         Pituicyte-derived tumours
              Pituicyte tumour family
         Neuronal tumours
              Gangliocytoma and mixed gangliocytoma - PitNET/pituitary adenoma
              Sellar neurocytoma

    Other sellar tumours

              Meningioma
              Chordoma

Thyroid gland

              Introduction

    Developmental abnormalities

              Thyroglossal duct cyst
              Other congenital thyroid abnormalities

    Follicular cell-derived neoplasms

         Benign tumours
              Thyroid follicular nodular disease
              Follicular thyroid adenoma
              Follicular thyroid adenoma with papillary architecture
              Oncocytic adenoma of the thyroid
         Low risk neoplasms
              Non-invasive follicular thyroid neoplasm with papillary-like nuclear features
              Thyroid tumours of uncertain malignant potential
              Hyalinizing trabecular tumour of thyroid
         Malignant neoplasms
              Follicular thyroid carcinoma
              Invasive encapsulated follicular variant papillary carcinoma
              Papillary thyroid carcinoma
              Oncocytic carcinoma of the thyroid
              Follicular-derived carcinomas, high-grade
              Anaplastic follicular cell derived thyroid carcinoma

    Thyroid C-cell derived carcinoma

              Medullary thyroid carcinoma

    Mixed medullary and follicular-cell derived carcinomas

              Mixed medullary and follicular cell-derived thyroid carcinoma

    Salivary gland-type carcinomas of the thyroid

              Mucoepidermoid carcinoma of the thyroid
              Secretory carcinoma of salivary gland type

    Thyroid tumours of uncertain histogenesis

              Sclerosing mucoepidermoid carcinoma with eosinophilia
              Cribriform morular thyroid carcinoma

    Thymic tumours within the thyroid

              Thymoma family
              Spindle epithelial tumour with thymus-like elements
              Thymic carcinoma family

    Embryonal thyroid neoplasms

              Thyroblastoma

Parathyroid glands

              Introduction
              Parathyroid hyperplasia
              Parathyroid adenoma
              Parathyroid lipoadenoma
              Atypical parathyroid tumour
              Parathyroid carcinoma

Adrenal gland

              Introduction

    Adrenal cortex

              Adrenal rests
              Adrenal cysts
              Adrenal myelolipoma
         Adrenal cortical tumours
              Congenital adrenal hyperplasia
              Adrenocortical nodular disease
              Adrenal cortical adenoma
              Adrenal cortical carcinoma
         Sex cord stromal and other tumours
              Adrenal sex cord stromal tumour
              Adenomatoid tumour
              Adrenal melanoma

Tumours of the adrenal medulla and extra-adrenal paraganglia

              Introduction
         Neuroblastic tumours
              Neuroblastoma
              Ganglioneuroblastoma, intermixed
              Ganglioneuroblastoma, nodular
              Ganglioneuroma
         Paraganglioma and pheochromocytoma
              Phaeochromocytoma
              Sympathetic paraganglioma
              Parasympathetic paraganglioma
         Composite paraganglion tumours
              Composite phaeochromocytoma and paraganglioma

Neuroendocrine pancreas

    Neuroendocrine neoplasms

              Introduction
         Neuroendocrine tumours
              Non-functioning (non-syndromic) neuroendocrine tumours
              Insulinoma
              Glucagonoma
              Somatostatinoma
              Gastrinoma
              VIPoma
              Serotonin-producing tumours with and without carcinoid syndrome
              Other pancreatic neuroendocrine tumours with ectopic hormone production
         Neuroendocrine carcinomas
              Pancreatic neuroendocrine carcinoma
         Mixed neuroendocrine-non-neuroendocrine neoplasms (MiNENs)
              Mixed ductal adenocarcinoma-neuroendocrine neoplasms
              Mixed acinar neuroendocrine carcinomas

Neuroendocrine neoplasms, non-endocrine organs

              Introduction

    Neuroendocrine neoplasms

         Neuroendocrine tumours
              Neuroendocrine tumour
         Neuroendocrine carcinoma
              Small cell neuroendocrine carcinoma
              Large cell neuroendocrine carcinoma
              Merkel cell carcinoma
         Mixed neuroendocrine neoplasms
              Mixed neuroendocrine-non-neuroendocrine neoplasms (MiNENs)
         Paragangliomas-like NEN
              Composite gangliocytoma/neuroma and neuroendocrine tumour (CoGNET)
              Cauda equina neuroendocrine tumour (previously paraganglioma)

Mesenchymal and stromal tumours

              Introduction
         Lipocytic tumours
              Lipoma
         Fibrous tumours
              Solitary fibrous tumour
         Vascular tumours
              Benign vascular tumours
              PEComa
              Glomangioma and glomus tumour
              Angiosarcoma
         Smooth muscle tumours
              Leiomyoma
              Leiomyosarcoma
         Skeletal muscle tumours
              Rhabdomyosarcoma family
         Peripheral nerve sheath tumours
              Schwannoma
              Neurofibroma
              Granular cell tumour
              MPNST

Haematolymphoid tumours

              Introduction
              IgG4-related disease
              Extranodal marginal zone lymphoma
              Diffuse large B cell lymphoma
              Langerhans cell histiocytosis
              Rosai Dorfman disease
              Erdheim Chester disease
              Follicular dendritic cell sarcoma

Germ cell tumours

         Germ cell tumours
              Introduction
              Germ cell tumours in endocrine organs
              Teratomas with endocrine differentiation

Metastasis

              Introduction
              Metastasis to the pituitary
              Metastasis to thyroid
              Metastasis to the adrenal

Genetic tumour syndromes

              Introduction
              Multiple endocrine neoplasia type 1
              Multiple endocrine neoplasia type 2
              Multiple endocrine neoplasia type 4
              Multiple endocrine neoplasia type 5 (MAX related tumours)
              Hyperparathyroidism jaw tumour syndrome
              Von Hippel Lindau syndrome
              SDH deficient tumour syndromes
              Neurofibromatosis type 1
              Carney complex
              McCune Albright syndrome
              DICER1 syndrome
              Glucagon cell hyperplasia and neoplasia
              MAFA related familial insulinomatosis
              Syndromic familial follicular cell-derived thyroid tumours
              Non-syndromic familial follicular cell-derived thyroid tumours